Section 14: Hematologic Disorders
The genetic inheritance pattern for hemophilia is:
The factor deficit in hemophilia B is:
Which of the following is not considered a goal of Hemophilia therapy?
A. Prevent bleeding episodes
B. Prevent long term complications
D. Arrest bleeding if it occurs
Patients with severe hemophilia have ______% factor activity level.
The first-line therapeutic approach to treating an active bleed in a patient with severe hemophilia without inhibitors is:
A. Plasma derived factor replacement
B. Recombinant factor replacement
C. Activated prothrombin complex concentrates (aPCCs)
Which is a true statement regarding prophylaxis therapy for hemophilia?
A. Not recommended by any national organization
B. Recommended approach but optimal dosing and schedule is not well defined
D. Patient compliance is not a factor in overall outcome
The most impactful therapeutic complication of therapy for hemophilia patients is: